Search on: STRIATONIGRAL DEGENERATION 
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Descriptor English:   Striatonigral Degeneration 
Descriptor Spanish:   Degeneración Estriatonigral 
Descriptor Portuguese:   Degeneração Estriatonigral 
Synonyms English:   Atrophies, Striatonigral
Atrophy, Striatonigral
Degeneration, Striatonigral
Striatonigral Atrophies
Striatonigral Atrophy
Striatonigral Degenerations  
Tree Number:   C10.177.575.550.875
C10.228.140.079.612.800
C10.228.662.550.800
Definition English:   A sporadic neurodegenerative disease with onset in middle-age characterized clinically by Parkinsonian features (e.g., MUSCLE RIGIDITY; HYPOKINESIA; stooped posture) and HYPOTENSION. This condition is considered a clinical variant of MULTIPLE SYSTEM ATROPHY. Pathologic features include a prominent loss of neurons in the zona compacta of the SUBSTANTIA NIGRA and PUTAMEN. (From Adams et al., Principles of Neurology, 6th ed, p1075-6) 
See Related English:   Parkinsonian Disorders
 
History Note English:   2000; use MULTIPLE SYSTEM ATROPHY 1998-1999 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   34222 
Unique Identifier:   D020955 

Occurrence in VHL:
 

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